L-α-Hydroxyglutaric acid disodium salt
SIAL/61313 - analytical standard
Synonym: (S)
CAS Number: 63512-50-5
Empirical Formula (Hill Notation): C5H6Na2O5
Molecular Weight: 192.08
MDL Number: MFCD00021700
Linear Formula: C5H6O5Na2
Product Type: Chemical
application(s) | clinical testing |
assay | ≥98.0% (GC) |
format | neat |
grade | analytical standard |
InChI | 1S/C5H8O5.2Na/c6-3(5(9)10 |
InChI key | DZHFTEDSQFPDPP-QTNFYWBSSA |
optical activity | [α]/D -8.5±1.5°, c = 1 in 0.1 M NaOH |
shelf life | limited shelf life, expiry date on the label |
SMILES string | [O-]C(CC[C@@H](C([O-])=O) |
storage temp. | 2-8°C |
Biochem/physiol Actions: | L-alpha-Hydroxyglutaric acid accumulates as a result of a rare defect in L-2-HG dehydogenase, leading to the metabolic disorder L-2-hydroxyglutaric aciduria (L-2HGA). L-2HGA is associated with neuronal defects, leukodystrophy and linked to an increased risk of brain tumors. |
RIDADR | NONH for all modes of transport |
WGK Germany | WGK 3 |
Flash Point(F) | Not applicable |
Flash Point(C) | Not applicable |
Purity | ≥98.0% (GC) |
Storage Temp. | 2-8°C |
UNSPSC | 41116107 |