3-Hydroxyisovaleryl-L-carnitine

SIAL/91298 - analytical standard

Synonym: (2R)-3-Carboxy-2-(3-hydroxy-3-methyl-1-oxobutoxy)-N,N,N-trimethyl-1-propanaminium inner salt

CAS Number: 99159-87-2
Empirical Formula (Hill Notation): C₁₂H₂₃NO₅
Molecular Weight: 261.31
Linear Formula: C₁₂H₂₃NO₅
Product Type: Chemical

Catalog Number	PKG Qty.	Price


45-91298-10MG	10 mg	$320.00 1/EA	Add To Favorites

Properties
Descriptions
Safety Info.
Basic Data

application(s)	clinical testing
assay	≥90.0% (HPLC)
format	neat
grade	analytical standard
impurities	≤15% water (calc. on elemental analysis)
InChI	1S/C12H23NO5/c1-9(2)6-11(16)18-12(17,7-10(14)15)8-13(3,4)5/h9,17H,6-8H2,1-5H3
InChI key	DHRNMNHPSWBJEN-UHFFFAOYSA-N
optical activity	[α]/D -17.0±2.0°, c = 0.1 in H₂O
Quality Level	100
shelf life	limited shelf life, expiry date on the label
SMILES string	C[N+](C)(C)C[C@H](OC(CC(C)(O)C)=O)CC([O-])=O
storage temp.	2-8°C

Biochem/physiol Actions:

3-Hydroxyisovaleryl-L-carnitine is an endogenous metabolite that can result from impairment in the leucine catabolic pathway. 3-Hydroxyisovaleryl-L-carnitine was observed in plasma and urine of patient with isolated 3-methylcrotonyl-CoA carboxylase deficiency and is used as biomarker of biotin deficiency in humans and other metabolic disorders.

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RIDADR	NONH for all modes of transport
WGK Germany	WGK 3
Flash Point(F)	Not applicable
Flash Point(C)	Not applicable

Purity	≥90.0% (HPLC)
Storage Temp.	2-8°C
UNSPSC	41116107

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