Butyryl-L-carnitine
SIGMA/42623 - ≥97.0% (TLC)
Synonym: (2R)-3-Carboxy-N,N,N-
CAS Number: 25576-40-3
Empirical Formula (Hill Notation): C11H21NO4
Molecular Weight: 231.29
MDL Number: MFCD01674827
Linear Formula: C11H21NO4
Product Type: Chemical
assay | ≥97.0% (TLC) |
color | white to off-white |
form | powder, crystals or chunks |
InChI | 1S/C11H21NO4/c1-5-6-11(15 |
InChI key | QWYFHHGCZUCMBN-SECBINFHSA |
optical activity | [α]/D -23±2°, c = 1 in H2O |
Quality Level | 100 |
SMILES string | C[N+](C)(C)C[C@H](OC(CCC) |
storage temp. | 2-8°C |
Application: |
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Biochem/physiol Actions: | Butyrylcarnitine is elevated in patients with Acyl-CoA dehydrogenase, short-chain (SCAD) deficiency, in infants with acute acidosis and generalized muscle weakness and in middle-aged patients with chronic myopathy localized in muscle; very long chain Acyl-CoA dehydrogenase deficiency, and celiac disease. |
RIDADR | NONH for all modes of transport |
WGK Germany | WGK 3 |
Flash Point(F) | Not applicable |
Flash Point(C) | Not applicable |
Purity | ≥97.0% (TLC) |
Storage Temp. | 2-8°C |
UNSPSC | 12352200 |